Congenital Cystic Adenomatoid Malformation
Treatment

Most babies with CCAM are treated with surgery soon after birth or several months later, depending on the severity of the CCAM. A small group of severe cases may be treated before birth with fetal intervention.

Most infants born with a CCAM have no symptoms at birth, although occasionally an infant may have difficulty breathing and will require oxygen and the use of a machine called a ventilator.

Infants with no symptoms at birth can go home after a few days in the hospital and return at 3 months of age for a CT scan. An operation to remove the CCAM may be scheduled after the pediatric surgeon and radiologist (a physician trained to read X-rays) review the results. CCAM removal is generally recommended because of the risk of lung infections and cancerous transformation later in life.

In most infants, the operation is done with tiny telescopic instruments though several very small incisions, instead of a single large chest incision. Your baby will stay in the hospital two to three days but probably will be released as soon as he or she is breathing easily, takes formula or breast milk well and is comfortable on pain medication given orally.

Fetal intervention is offered only when there is evidence of heart failure in the fetus. The procedure involves an operation for the mother, like a Caesarean section, in which a fetal surgeon removes the CCAM from the fetus' chest.

Reviewed by health care specialists at UCSF Benioff Children's Hospital.

Related Information

UCSF Clinics & Centers

Surgery Clinic
400 Parnassus Ave., Suite A123
San Francisco, CA 94143
Phone: (415) 476-2538
Fax: (415) 476-2929
Appointment information

Fetal Treatment Center
400 Parnassus Ave., A123
San Francisco, CA 94143
Phone: (415) 476-0445
Fax: (415) 502-0660
Appointment information